Multiple biliary hamartomatosis

Authors

  • Roberto Pérez Menéndez Hospital Hermanos Ameijeiras Servicio de Gastroenterologìa https://orcid.org/0000-0002-4964-3651
  • Pedro Evelio Velbes Marquetti Hospital Hermanos Ameijeiras Servicio de Gastroenterologìa

Keywords:

Hamartomatosis biliar múltiple, laparoscopia, biopsia hepática.

Abstract

Introduction: Multiple biliary hamartomatosis or von Meyenburg complex disease was described by this author in 1955. Its origin is dysembryogenic with a benign and asymptomatic evolutionary course, with normal liver function tests. Imaging studies can confirm the diagnosis, but likewise, when it is a multinodular liver, chronic liver disease can be diagnosed without specifying its etiology, which is why it is essential a histological diagnosis with a directed overlaparoscopic liver biopsy. No specific treatment is needed and its follow-up is semi-annual or annual ultrasound.

Objective: To present the value of laparoscopically directed liver biopsy for multiple biliary hamartomatosis lesions.

Case report: A 53-year-old patient with a history of being a social drinker with a weekly frequency is reported. He was admitted for fever associated with urinary sepsis, in which a fortuitous ultrasound finding of a multinodular liver appeared, without requiring an etiological diagnosis by other imaging studies. This led to a laparoscopy with a liver biopsy aimed at the observed lesions. The histological diagnosis of this entity is confirmed.

Conclusions: The importance and validity of the diagnostic value of laparoscopy, as well as directed liver biopsy to achieve a certain histological diagnosis in this entity, was demonstrated.

 

Keywords: multiple biliary hamartomatosis; laparoscopy; liver biopsy.

 

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Author Biographies

Roberto Pérez Menéndez, Hospital Hermanos Ameijeiras Servicio de Gastroenterologìa

Especialista en 2do grado en Gastroenterologia. Profesor e investigador auxiliar. Hospital Clinico Quirurgico Hermanos Ameijeiras

Pedro Evelio Velbes Marquetti, Hospital Hermanos Ameijeiras Servicio de Gastroenterologìa

Especialista en 2do grado en Gastroenterologia. Profesor e investigador auxiliar. Hospital Clinico Quirurgico Hermanos Ameijeiras

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Published

2021-12-14

How to Cite

1.
Pérez Menéndez R, Velbes Marquetti PE. Multiple biliary hamartomatosis. Rev Cubana Med [Internet]. 2021 Dec. 14 [cited 2025 Dec. 13];60(4). Available from: https://revmedicina.sld.cu/index.php/med/article/view/1674

Issue

Vol. 60 No. 4 (2021): octubre-diciembre

Section

Case Reports

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